Citation

Demirozu ZT, Kucukaksu DS. Turkiye Klinikleri Cardiovascular Sciences 2015; 27(1): 36-42.

Copyright

(Copyright © 2015)

DOI

10.5336/cardiosci.2014-42264

PMID

unavailable

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) usually originates from right ventricle, has a prevalence 1 in 1000 and leading cause of death in people aged less than 35 years of age, also desmosome mutations and family history can be seen in this disease. We reviewed the literature and described three patients with arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C). They had T wave inversion in chest leads V1 to V4 and had premature ventricular complexes of left bundle branch block and left axis deviation, or right bundle branch block (RBB) had implantable cardioverter defibrillator (ICD) implantation and fulfilled the task force criteria for diagnosis of ARVD/C. One patient had familial erythrocytosis and thrombus formation in the right atrium and the right ventricle. He was listed as status 1A and had 2 times phlebotomy during the hospitalization. The other patient had warfarin intoxication, and had hepatic congestion due to end-stage right heart failure. The third patient had a history of cerebrovascular event and had a family history of ARVD/C. All of our patients had the medical regimen for the management of ARVD/C. All of the patients were in NYHA Class III-IV while they admitted to our clinic and they had their final therapeutic option as an orthotopic heart transplantation and have a good quality of life. © 2015 by Turkiye Klinikleri.

Language: en

Keywords

adult; human; female; male; case report; quality of life; psychotherapy; liver failure; suicide attempt; treatment outcome; emotional disorder; mental disease; disease classification; anticonvulsive agent; drug intoxication; human tissue; recurrent disease; anticoagulant agent; grief; cyanosis; tonic clonic seizure; follow up; hospital discharge; drug withdrawal; postoperative period; antibiotic agent; warfarin; heart transplantation; phlebotomy; dyspnea; coughing; Heart transplantation; heart palpitation; heart catheterization; heparin; treatment response; extubation; heart ventricle tachycardia; focal epilepsy; muscle atrophy; Article; diuretic agent; tracheostomy; heart ventricle extrasystole; international normalized ratio; heart left ventricle ejection fraction; psychosocial rehabilitation; drug substitution; transthoracic echocardiography; hemiparesis; hepatomegaly; breathing exercise; lung lavage; peripheral edema; respiratory acidosis; heart right bundle branch block; heart atrium fibrillation; heart right ventricle dysplasia; young adult; heart atrium enlargement; systolic heart murmur; pneumocystosis; hematocrit; liver congestion; Holter monitoring; T wave inversion; cell degeneration; faintness; familial disease; heart muscle biopsy; fibrosing alveolitis; mental disease assessment; tricuspid valve regurgitation; Arrhythmogenic right ventricular dysplasia; cardiovascular magnetic resonance; diuretic therapy; erythrocytosis; heart atrium thrombosis; heart left bundle branch block; heart right ventricle failure; heart ventricle thrombosis; implantable cardioverter defibrillator; lung aspiration; methicillin-resistant Staphylococcus epidermidis