TY - JOUR PY - 2016// TI - Development of new forms of self-injurious behavior following total dental extraction in Lesch-Nyhan disease JO - Nucleosides, nucleotides, and nucleic acids A1 - Gisbert de la Cuadra, Livia A1 - Torres, Rosa J. A1 - Beltrán, Luis M. A1 - Sánchez, Arantxa A1 - Puig, Juan G. SP - 524 EP - 528 VL - 35 IS - 10-12 N2 - We report two Lesch-Nyhan Disease (LND) patients who developed new forms of self-injurious behavior following total dental extraction. Patients 1 and 2 were submitted to total teeth extraction at the age of 13 and 8 years, respectively, due to continuous self-biting, not prevented by mouth guards. Severity of dystonia was markedly reduced and quality of life improved. After 12 and 17 months, respectively, patient 1 started rubbing one foot against other and scratching toenails with his hands, and patient 2 stuck his legs and feet against hard objects. These forms of self-injury behavior could be easily prevented with protective materials, according to the mothers.

Language: en

LA - en SN - 1525-7770 UR - http://dx.doi.org/10.1080/15257770.2016.1184276 ID - ref1 ER -